Neurofibromatosis type 1-associated intrathoracic meningocele management with a novel surgical method: A case report and review of the literature

نویسندگان

  • Zhao-Wen Cai
  • Wei Zhao
  • Ran-Ze Cai
  • Chun-Mei Chen
  • Chun-hua Wang
چکیده

Neurofibromatosis type-1 (NF-1) associated-intrathoracic meningocele is a rare clinical finding. We report the cases of two adults who were diagnosed with NF-1-associated intrathoracic meningoceles and successfully treated with a novel surgical technique called “dural turnover repair method.” Both patients were symptomatic. Preoperative imaging showed a cystic lesion in the thoracic cavity of both patients. Their symptoms were relieved and the cysts were markedly diminished postoperatively. Neither patient experienced complications from the operation. We wish to emphasize that the novel “dural turnover repair method” is effective in the treatment of intrathoracic meningocele associated with NF-1.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

A Large Intrathoracic Mass in a Patient with Neurofibromatosis-1: a case report

Abstracts: Dural ectasia is circumferential expansion or dilatation of the dural sac, and has been frequently reported in association with type 1 neurofibromatosis (NF1). It should be differentiated from posterior mediastinal tumors such as neurofibroma, neuroblastoma, and ganglioneuroma because NF-1 has a high risk of tumor formation. In the spinal deformities of NF-1 patients, despite the sco...

متن کامل

Giant intrathoracic meningoceles associated with cutaneous neurofibromatosis type I: case report.

BACKGROUND Intrathoracic meningocele is a rare pathology, almost always associated with neurofibromatosis type I and with a few cases related in the literature. In the majority of cases cysts are small or asymptomatic, and the surgery is indicated when big or symptomatic cysts are present. We report a case of giant intrathoracic cysts surgically extirpated through out thoracotomy. CASE A 59-y...

متن کامل

Massive Spontaneous Hemothorax, Giant Intrathoracic Meningocele, and Kyphoscoliosis in Neurofibromatosis Type 1

Neurofibromatosis type 1 (NF-1) is a heterogeneous autosomal dominant disease with an incidence ranging from 1 in 2500 to 1 in 3000. Rare intrathoracic vascular disorders resulting in massive spontaneous hemothorax with fatal consequences may occur in these patients, so also are various types of skeletal dysplasia which may result in dramatic presentations, posing management challenges to the a...

متن کامل

Collaborative treatment of huge intrathoracic meningoceles associated with neurofibromatosis type 1: a case report

BACKGROUND An intrathoracic meningocele is a relatively rare disease, and it commonly accompanies neurofibromatosis type 1. Patients tend to have no symptom but if its size is too large and compresses a lung and neighboring organs, it needs shunt drainage or surgical resection. CASE PRESENTATION Herein, we present the case of a 52 year-old female patient with huge intrathoracic meningoceles a...

متن کامل

Isolated true anterior thoracic meningocele.

Intrathoracic meningocele is rare and is usually associated with neurofibromatosis type I. Most of the reported thoracic meningoceles are not strictly anterior in location, but also lateral or anterolateral. We report a case of true anterior thoracic meningocele with no associated generalized mesenchymal dysplasia.

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:

دوره   شماره 

صفحات  -

تاریخ انتشار 2017